Background: Non-rhabdomyosarcoma soft tissue sarcomas (NRSTS) represent a rare and diverse group of over 50 histological subtypes with poor outcomes, particularly in advanced stages or delayed diagnosis. Despite advancements in pediatric oncology, there is a significant gap in localized data regarding survival outcomes and associated risk factors for NRSTS. Objective: This study aims to evaluate survival outcomes and identify key risk factors among patients diagnosed with NRSTS. Methods: A retrospective review was conducted on 44 patients diagnosed with NRSTS at King Fahad Specialist Hospital-Dammam (KFSHD) from 2008 to 2020. Clinical data were extracted from cancer registries and patient records, including tumor characteristics, treatment modalities, and survival outcomes. Kaplan-Meier analysis was employed to assess survival rates. Results: The overall survival rate for the entire group at five years was about 70%. Patients who had surgery-maintained survival rates above 75% over five years, while individuals deemed surgically unresectable, exhibited a survival rate of around 25%. Similarly, patients who received radiotherapy had nearly 90% survival at five years, compared to those who did not. Conclusion: Our findings suggest that surgery and radiotherapy are associated with improved survival outcomes, with substantial benefits observed in patients undergoing either treatment highlighting the importance of local control in NRST .