Background: Primary malignant lymphomas (PHML) of the larynx are exceptional. Case: A 43-year-old man presented with dysphonia and pulmonary aspiration. The physical examination found bilateral cervical lymph nodes and the pan endoscopy revealed a bleeding budding tumor of the epiglottis. The head and neck scan showed a mass arising from the epiglottis and invading the vallecules, the right aryepiglottic fold, the two vocal cords and the anterior commissure with bilateral cervical lymph nodes. The patient inderwent a chemotherapy, followed by an irradiation of the involved nodal fields and the initial laryngeal tumor. At a follow-up time of 3.5 years, the patient remains in disease complete remission. Conclusion: We report the first case of laryngeal PHML. Given the lack of recommendations for this extremely rare type of tumor. The prognosis, even if it seems to be good, it is difficult to specify whether it matches that of other localizations or not. Keywords: Laryngeal Tumors, Malignant Hodgkin Lymphoma, head and neck, Chemotherapy, Radiotherapy