Hailey- Hailey Disease:- insights from a clinical casePrashant Bhatta1,Pramod  kumar Kafle2, Ramesh Khadayat1, Utsav Dulal3, Amrit Bhattarai2, Gaurab Khadka2,Sagar Rana Magar11. Patan Academy of Health Sciences, Patan Hospital, Lalitpur2. Madhyabindu District Hospital3. B.P. Koirala Institute of Health Sciences, DharanCorresponding author:- Ramesh KhadayatEmail:- rameshkhadayat123@gmail.com

Authors details:1. Somee Rauniyar (Corresponding Author)Affiliation: Madan Bhandari Institute of Health Sciences (Hetauda Hospital), Makawanpur, NepalContribution: Conceptualization, Data curation, Formal Analysis, Investigation, Methodology, Project Administration, Resources, Supervision, Validation, Writing-original draft, Writing-review & editingSupervision, Writing- Original draft, Writing-review, and editingOrcid No: 0009-0007-5466-3183Email: rauniyarsomee4@gmail.com2. Deepak SubediAffiliation: Nepalese Army Institute of Health Sciences College of Medicine,Kathmandu, NepalContribution: Data curation, Formal Analysis, Investigation, Methodology, Supervision, Writing-original draft, Writing-review, and editingOrcid No: 0000-0001-8512-1482Email: subedideepak28@gmail.com3. Bishwodip BaralAffiliation: Sukraraj Tropical and Infectious and Disease Hospital, KathmanduContribution: Formal Analysis, Investigation, Methodology, Resources, Supervision, Validation, Writing-review, and editingOrcid No: 0000-0002-2066-7940Email: bishwodipbaral@gmail.com4. Pramod kumar KafleAffiliation: Chitwan Medical College and Teaching Hospital, Chitwan, NepalContribution: Data curation, Formal Analysis, Investigation, Methodology, Resources, Writing-review, and editingOrcid No: 0000-0003-3945-7190Email: pramodkafle18@gmail.com5. Neha BistaAffiliation: Madan Bhandari Institute of Health Sciences (Hetauda Hospital), Makawanpur, NepalContribution: Investigation, Methodology, Supervision, Validation, Writing-review, and editingWriting- Writing-review and editingOrcid No: 0009-0009-1934-6347Email: nehabista992@gmail.com6. Prajwal SapkotaAffiliation: Madan Bhandari Institute of Health Sciences (Hetauda Hospital), Makawanpur, NepalContribution: Formal analysis, Methodology, Resources, Writing-review, and editingOrcid No: - 0009-0009-5933-5837Email: dr.prajwalsapkota@gmail.com

Pachydermoperiostosis (PDP) is a rare genetic disorder with unclear etiopathogenesis. We report a case of a 38-years-old male who presented with classic features of PDP. Patient showed a good initial response to Etoricoxib therapy but the safety and efficacy over long-term use are yet to be determined in further studies.