Anomalous aortic origin of the coronary arteries (AAOCA) is a rare congenital abnormality involving the origin and course of coronary arteries and present with diverse clinical manifestations in patients. We describe a 12-year-old male patient whose anomalous left coronary artery (LCA) originated from the right aortic sinus of Valsalva (RASV), accompanied with myocardial infarction. He was diagnosed by multimodal imaging including invasive coronary angiography (ICA), computed tomography angiography (CTA) and transthoracic echocardiography (TTE), providing morphologic and functional information of the abnormal coronary arteries. The patient was corrected with surgery after the preparation of multimodal imaging.