Congenital self-healing reticulohistiocytosis of Hashimoto and Pritzker (CSHR), a form of Langerhans Cell Histiocytosis (LCH), is a rare benign proliferative disorder that typically self-resolves at 6 months. We present an atypical case of CSHR with first onset at 10 months of age which showed histologic features of LCH.