The median solitary maxillary central incisor syndrome (SMMCI) is a rare developmental disorder consisting of multiple defects found on the body midline. The aim of this report was to describe multiple craniofacial features of a 10-years-old girl presented with SMMCI, and discuss the dental treatment alternatives in such young patients.

Lymphangiomas of the tongue are very rare tumors usually diagnosed in infancy and early childhood. Children with Lymphangiomas of the tongue may require multidisciplinary care and a close collaboration between physician and dentist to be able to eradicate any sources of dental infections before undertaking medical treatment.