Hypertrophic cardiomyopathy (HCM) typically involves the left ventricle. While right ventricular hypertrophy may occasionally coexist, severe right ventricular hypertrophy or right ventricular outflow tract (RVOT) obstruction is rare, with unclear incidence. Isolated right ventricular HCM has only been reported in individual cases. Here, we present a case of RVOT-type HCM.