Quadricuspid aortic valve (QAV) is a rare congenital anomaly. There are various hypotheses regarding the embryological development of a QAV. Patients are usually diagnosed at a mean age of 50.7 years with a male preponderance and a surgery in the form of an aortic valve repair or replacement is usually the treatment strategy. There are various congenital cardiac defects and anomalies associated with a QAV which can be coronary artery abnormalities, ASD, VSD etc. We are reporting a 51-year-old female patient who was incidentally diagnosed with a quadricuspid aortic valve and progressive aortic regurgitation with coronary artery disease.