Colorectal cancers are commonly seen in adults but seldom reported in children. An 11-year-old child presented with massive ascites and abdominal pain abdomen. On evaluation, abdominal imaging showed diffuse thickening of the sigmoid colon along with the rectum. Colonoscopic biopsy revealed signet cell variant of mucinous adenocarcinoma of colon. Treatment involves surgical resection, however chemotherapeutic drugs may be used for palliative cases. Pediatric colorectal carcinomas are associated with poor prognosis as they present at a more advanced stage[(1)](#ref-0001). Signet cell carcinomas are associated with an poor prognosis across age groups.[(2)](#ref-0002) This report intends to discuss this rare pediatric malignancy.