Conclusion (110 words):
This article presents a rare case of a patient with ADPKD suffering from
both a myxoid liposarcoma and a PPGLs. Based on radiological findings
and the patient’s history of severe hypertension, the lesion adjacent to
the left kidney was identified as a paraganglioma. While hypertension is
a common clinical feature in patients with ADPKD, this case highlights
the necessity of systematically investigating secondary causes,
particularly in cases of refractory or difficult-to-control
hypertension. This case illustrates how an apparently straightforward
clinical diagnosis can obscure a potentially serious underlying
condition. Further research should explore the prevalence and optimal
screening protocols for neuroendocrine tumours in ADPKD, to enhance
diagnostic accuracy and patient outcomes.