Introduction:Takayasu arteritis (TA), also known as pulseless disease, is a rare systemic inflammatory condition that primarily affects the medium and large arteries, including their branches. It predominantly occurs in young Asian women, with a reported worldwide incidence of only 1 to 2 per million people1.Women are more frequently affected than men2, with a varying incidence rate in different parts of the globe. Male to female ratio is 1:8 in western countries and 1:3 in Japan3.It is a chronic disease primarily impacting the aorta and its large branches. Early diagnosis is crucial to prevent severe end organ damage, including stroke and ischemic heart disease4.However, diagnosis is often challenging due to the non-specific systemic inflammatory symptoms present in the early phase, which can lead to an insidious clinical course until vascular ischemic complications emerge5.The disease typically progresses through two phases: an initial pre-occlusive inflammatory phase that may go unnoticed, followed by an occlusive phase characterized by ischemic vascular symptoms resulting from arterial lesions such as stenosis, occlusion, or aneurysm6.Extremity pain, claudication, bruits, pulselessness and unrecordable blood pressure are the common features of patient visiting health care facility. However, presentation with acute visual loss or stroke may be particularly rare7.18% of patients with large vessel vasculitis presents with unilateral visual loss at diagnosis, often resulting in irreversible damage. Early administration of pulsed intravenous methylprednisolone may provide some benefit to patients experiencing early onset of visual symptoms8.While numerous systematic reviews have explored ocular manifestations in various systemic diseases, few have focused on the eye involvement in Takayasu arteritis.