Introduction:
Fahr’s disease, named after German neurologist Karl Theodor Fahr, was
first reported in 1930. This rare neurological condition is
characterized by abnormal calcium deposits in the basal ganglia,
thalamus, dentate nuclei, and subcortical white matter. It is commonly
inherited in about 60% of diagnoses in an autosomal dominant manner
(Amisha and Munakomi 2023).
The symptoms of Fahr disease, also known as bilateral
striatopallidodentate calcinosis, dysarthria seizure, involuntary
movements, headaches, dementia, and vision impairment
(Rissardo, Caprara et al.
2019Bhandari, Ghimire et al. 2023, ).
This syndrome can present differently in each patient, and there is no
clear correlation between the brain lesion and the clinical symptoms
(Amisha and Munakomi 2023).