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Pediatric atypical teratoid/rhabdoid tumor in the cauda equina with rapid tumor progression: A case report and review of the literature
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  • Makoto Ohno,
  • Takahiro Tsuchiya,
  • Yuko Watanabe,
  • Shohei Fujita,
  • Bunpei Miyazaki,
  • Hirokazu Sugino,
  • Hiroshi Igaki,
  • Akihiko Yoshida,
  • Masamichi Takahashi,
  • Shunsuke Yanagisawa,
  • Sho Osawa,
  • Chitose Ogawa,
  • Yoshitaka Narita
Makoto Ohno
Kokuritsu Gan Kenkyu Center Chuo Byoin

Corresponding Author:mohno@ncc.go.jp

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Takahiro Tsuchiya
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Yuko Watanabe
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Shohei Fujita
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Bunpei Miyazaki
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Hirokazu Sugino
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Hiroshi Igaki
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Akihiko Yoshida
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Masamichi Takahashi
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Shunsuke Yanagisawa
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Sho Osawa
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Chitose Ogawa
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Yoshitaka Narita
Kokuritsu Gan Kenkyu Center Chuo Byoin
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Abstract

Atypical teratoid/rhabdoid tumors (AT/RT) rarely occur in the cauda equina; thus, the clinical behavior and optimal treatment remain unclear. A 9-year-old boy presented with a rapidly progressing intradural extramedullary tumor at the L2–5 level, underwent tumor resection, and was diagnosed with AT/RT. His gait disturbance improved postoperatively, and he received adjuvant chemotherapy and radiotherapy. In 5 months of follow-up, recurrence was not observed. Although extremely rare, AT/RT should be included in the differential diagnosis, as it requires prompt therapeutic intervention. Safe resection with minimal functional impairment, followed by postoperative chemoradiation, can lead to tumor control and improve neurological function.