Restrictive cardiomyopathy is rare and usually associated with myocardium amyloidosis, which often involves multiple organs. Here, we describe a rare case of restrictive cardiomyopathy with myocardium amyloidosis. The diagnosis was established using electrocardiogram, transthoracic echocardiography, and confirmed using cardiac magnetic resonance imaging. Nevertheless, no evidence of involvement of the other organs was observed.