Introduction:
Primary Sjögren’s syndrome(pSS) is an idiopathic, autoimmune disorder
characterized by both localized and systemic manifestations. The most
common clinical presentations include the “sicca” or “dryness”
symptoms such as xerostomia and keratoconjunctivitis sicca due to
diminished salivary gland and lacrimal gland function, respectively.
Patients may also present with nonspecific symptoms such as fatigue and
arthralgia, as well as pulmonary, gastrointestinal, neurological and
renal involvement.1 Secondary Sjogren’s syndrome can
coexist with other autoimmune disorders such as rheumatoid arthritis
(RA) and systemic lupus erythematosus (SLE). 2
According to literature, ocular signs and symptoms in pSS range from
foreign body sensations, punctate or filamentous keratitis, to overt
seborrheic blepharitis and eyelid swelling is reported to be
rare.3 We report an usual/rare presentation of
Sjogren’s syndrome in which the patient developed severe evolving
mechanical ptosis and eyelid swelling to the extent that it impaired her
ability to lift open her eyes and see, along with a positive
anti-acetylcholine receptor antibody test.