Introduction
In 1971 Gianotti et al. first described benign cephalic histiocytosis (BCH) and up to the present approximately 70 cases have been reported in the literature. (1, 2) BCH belongs to the group of non-Langerhans cell histiocytoses (NLCH) and clinically and histologically resembles juvenile xanthogranuloma (JXG) and generalized eruptive histiocytosis (GEH). Skin lesions are characterized by erythematous, yellowish to brownish macules and papules, which are mostly located on head and neck. The etiology of BCH is as yet unresolved.