Abstract:
A 11-year-old female patient with tuberous sclerosis presented with
retinal hamartomas at different stages of evolution in the optical
coherence tomography with Sweep Source technology (OCT-SS). The right
eye presented with three lesions spectra. Lesion 1, at an earlier stage,
maximum thickness (MT) of 336 μm, preserved inner nuclear and inner
plexiform layers and disorganization of the ganglion cell layer. Lesion
2, MT of 438 μm and disorganization of the ganglion cell, inner nuclear
and inner plexiform layers, but outer plexiform layer apparently
preserved. Lesion 3, a hyperreflective dome-shaped proliferation with
posterior shadow, MT of 1478 μm, presented “moth-eaten” empty optical
spaces, with an apparent complete rupture of the retinal anatomy. In the
left eye, the lesion had a MT of 342 μm, preserved the retinal anatomy,
located at the level of the retinal nerve fiber layer, and identifiable
ganglion cell layer.