Introduction
Solitary Fibrous tumours (SFTs) were first described in 1931 by
Klemperer et al. as pleural tumours. Since then, it has been reported in
many extra-pleural sites but is found to be exceedingly rare. Most of
them are reported to arise from the pleura, and only 30% are of
extra-pleural origins. Less than a hundred cases of Primary
Retroperitoneal Solitary Fibrous Tumours have been described till now.
These are rare soft-tissue sarcomas, with mesenchymal origins. The
symptoms of these tumours depend on the location. The diagnosis is done
mainly by imaging such as ultrasonography, Computed tomography or
Magnetic resonance imaging. The standard of treatment for these tumours
is by surgical excision with clear margins. The role of adjuvant
chemotherapy is controversial.