Introduction:CNS embryonal tumors are highly malignant undifferentiated or poorly differentiated tumors of neuroepithelial origin, they take origin from embryonic cells that remain in the brain after birth, These tumors tend to spread through the cerebrospinal fluid (CSF) to other parts of the brain and spinal cord.Central nervous system embryonal tumor, not otherwise specified (NOS) was previously called primitive neuroectodermal tumors (PNET), these are rare tumors that form in the brain and spinal cord. (1)We describe CNS (NOS) that arose in the occipital lobe of a 27 year old patient.