Introduction:
Pulmonary artery sling (PAS) is a condition in which one of the branch pulmonary arteries originates from the contralateral sided pulmonary artery. Pulmonary artery sling was first described by Glaevecke and Doehle in 1897.1 The disease spectrum ranges from asymptomatic state to severe life-threatening airway obstruction requiring high pressure mechanical ventilation, or in extreme cases, extracorporeal support. A “ring-sling” complex describes when there is a congenital anomaly of the major airways including complete tracheal rings with tracheal stenosis and an associated pulmonary artery sling. Morbidity and mortality are related to the extent of airway involvement including tracheobronchial stenosis, lung development, genetic, cardiac comorbidities and the need for intensive care unit admission preceding the surgery.1,2 In more complex cases with long segment tracheal stenosis, diagnostic workup and airway surgery may require a highly specialised complex airway service and multidisciplinary team approach for optimal results.3-7