Adults (n =41) Adolescents 12-18 yrs (n =10)
Mean (SD), range
Age in years 32.7 (12.6), 19-71 14.2 (1.6), 12-17
Gender, % female 66% 70%
Genetic mutation (n %)
F508del/F508del 21 (51.2) 10 (100)
F508del/other 13 (31.7)
Other 7 (17.1)
Use of CFTR-modulator(s) (n %) 28 (68.3) 9 (90)
Symkevi 2 (4.9)
Orkambi 1 (2.4)
Kaftrio/Trikafta 22 (53.7) 8 (80)
Kalydeco 1 (2.4)
Combination of Kaftrio/Trikafta & Kalydeco 2 (2.4) 1 (10)
No 13 (31.7) 1 (10)
Pancreatic function (n %)
Sufficient 6 (14.6) 1 (10)
Insufficient, Endocrine 4 (9.8)
Insufficient, Exocrine 16 (39) 9 (90)
Insufficient, Both endocrine and exocrine 15 (36.6)
Mean FEV1 in % of predicted (SD) 72.1 (23.8) 83.6 (15.90)
BMI 22.2 (2.6), 18.6-28.4 20.2 (2.2), 17.1-24.4
Highest level of education N (%)
Low/Middle/High1 9 (23)/21 (54)/9 (23) 1 10 (100)
Average working hours per weekᶲ N (%)
0 17 (42) NA
1-12 6 (15) NA
13-24 7 (17) NA
> 25 9 (22) NA
Unknown 2 (5) NA
Relational status ᶲ
Single 21 (51) NA
Married 10 (24) NA
Living together with partner 10 (24) NA
Use of medication other than CF medication
Yes 14 (34) 2 (20)
No 27 (66) 8 (80)
Sport N (%)
Yes 30 (76) 7 (70)
No 10 (24) 3 (30)
Unknown 1 (2)
Probiotic N (%)
Yes 11 (27) 0 (0)
No 30 (73) 10 (100)