Demographic and clinical variables
Variables such as age, gender, type of CFTR mutation, Body
Mass Index (BMI), and pancreatic sufficiency were obtained from
pwCF using a demographic questionnaire which was then verified with the
medical record. Lung function (Forced expiratory volume in one second)
was assessed using the Masterscreen ( Jaeger®, CareFusion
Corporation) during clinical visits. Before assessing lung function,
short or long acting β2-adrenergic agonists were stopped
for 12 hours.