INTRODUCTION:
Primary synovial Chondromatosis (PSC), also called Reichel syndrome, is a benign tumor with cartilaginous nodules in the synovium joints. It usually affects diarthrodial joints and occurs between the third and fifth decade of life [5,7,17]. The glenohumeral joint is an unusual location in PSC, particularly in pediatric patients [4,7,16]. To our knowledge, there are only 5 cases of children reported in the literature. Herein, we report a rare case of PSC in a 14-year-old boy with an uncommon localization in the shoulder revealed by the chronic pain and the limited motion in the right arm. We also discuss clinical presentation, imaging findings and treatment of this rare condition in children based on current literature.