INTRODUCTION:
Primary synovial Chondromatosis (PSC), also called Reichel syndrome, is
a benign tumor with cartilaginous nodules in the synovium joints. It
usually affects diarthrodial joints and occurs between the third and
fifth decade of life [5,7,17]. The glenohumeral joint is an unusual
location in PSC, particularly in pediatric patients [4,7,16]. To our
knowledge, there are only 5 cases of children reported in the
literature. Herein, we report a rare case of PSC in a 14-year-old boy
with an uncommon localization in the shoulder revealed by the chronic
pain and the limited motion in the right arm. We also discuss clinical
presentation, imaging findings and treatment of this rare condition in
children based on current literature.