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A Nine-Year-Old Male with Barth Syndrome and Cardiac Transplant Presenting with Hyperviscosity Syndrome caused by EBV-Negative Plasmacytoid PTLD
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  • Yixian Li,
  • Adit Tal,
  • Rachel Offenbacher,
  • Nicolas Corral,
  • Neha Bansal,
  • Juan Ding,
  • Lisa Gennarini,
  • Leanne Ostrodka
Yixian Li
Children's Hospital at Montefiore

Corresponding Author:yli14@montefiore.org

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Adit Tal
Children's Hospital at Montefiore
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Rachel Offenbacher
Children's Hospital at Montefiore
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Nicolas Corral
Children's Hospital at Montefiore
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Neha Bansal
Children's Hospital at Montefiore
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Juan Ding
Montefiore Medical Center
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Lisa Gennarini
Children's Hospital at Montefiore
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Leanne Ostrodka
Children's Hospital at Montefiore
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Abstract

Posttransplant lymphoproliferative disorder is a rare but well-known complication in solid organ or hematopoietic transplant recipients secondary to immunosuppression. It can range from a cellular hyperplasia to a classic lymphoma. We describe a case of a nine-year-old male with Barth syndrome and a history of cardiac transplantation who developed plasmacytoid EBV-negative PTLD, an extremely rare entity in the pediatric population, and the evolvement of his PTLD to a more aggressive plasma cell neoplasm.