A Nine-Year-Old Male with Barth Syndrome and Cardiac Transplant
Presenting with Hyperviscosity Syndrome caused by EBV-Negative
Plasmacytoid PTLD
- Yixian Li
, - Adit Tal
, - Rachel Offenbacher
, - Nicolas Corral,
- Neha Bansal,
- Juan Ding,
- Lisa Gennarini,
- Leanne Ostrodka
Yixian Li
![](https://d197for5662m48.cloudfront.net/assets/icons/omniauth/orcid-ca37582cd91a671ed5cec57770e0e96c01b4b79b8b5b75d8598fc1ddac18c974.svg)
Children's Hospital at Montefiore
Corresponding Author:yli14@montefiore.org
Author ProfileAbstract
Posttransplant lymphoproliferative disorder is a rare but well-known
complication in solid organ or hematopoietic transplant recipients
secondary to immunosuppression. It can range from a cellular hyperplasia
to a classic lymphoma. We describe a case of a nine-year-old male with
Barth syndrome and a history of cardiac transplantation who developed
plasmacytoid EBV-negative PTLD, an extremely rare entity in the
pediatric population, and the evolvement of his PTLD to a more
aggressive plasma cell neoplasm.