Conclusion
Congenital lobar emphysema is a diagnostic challenge, and the confusion
can be further augmented in the presence of an obvious large congenital
heart defect. A close look over the chest X-ray may give the lead, but
the CT scan is a confirmatory investigation. Regular follow-up and a
high index of suspicion are necessary for early diagnosis. Lobectomy can
lead to dramatic improvement and is well tolerated.