Introduction
Hereditary hemorrhagic telangiectasia (HHT) (also known as Osler Weber
Rendu syndrome (OWRS)) is a rare dominant autosomal disorder with a
frequency of 6.1 to 12.1 per 100,000 (1). There are no differences
between genders. It is clinically characterized by telangiectasia,
recurrent epistaxis, visceral vascular lesions (arteriovenous
malformations - AVMs). Usually a person with HHT has a family history of
the disorder. This article reports a case that is clinically compatible
with this rare entity.