Introduction
Hereditary hemorrhagic telangiectasia (HHT) (also known as Osler Weber Rendu syndrome (OWRS)) is a rare dominant autosomal disorder with a frequency of 6.1 to 12.1 per 100,000 (1). There are no differences between genders. It is clinically characterized by telangiectasia, recurrent epistaxis, visceral vascular lesions (arteriovenous malformations - AVMs). Usually a person with HHT has a family history of the disorder. This article reports a case that is clinically compatible with this rare entity.