loading page

Absent Pulmonary Valve with L-Transposition of Great Arteries: A Case report
  • +3
  • Wataru Sakai,
  • Hidetsugu Asai,
  • Takafumi Oyasu,
  • Yosuke Arai,
  • Noriyoshi Ebuoka,
  • Jun Oba
Wataru Sakai
Hokkaido Medical Center for Child Health and Rehabilitation

Corresponding Author:sakaiwataru1128@gmail.com

Author Profile
Hidetsugu Asai
Hokkaido Daigaku
Author Profile
Takafumi Oyasu
Hokkaido Medical Center for Child Health and Rehabilitation
Author Profile
Yosuke Arai
Hokkaido Daigaku
Author Profile
Noriyoshi Ebuoka
Hokkaido Daigaku
Author Profile
Jun Oba
Hokkaido Daigaku
Author Profile

Abstract

Absent pulmonary valve syndrome and L-transposition of the great arteries are rare congenital anomalies. To our knowledge, patients with both have not been previously reported. We present a case of surgical success in the patient with absent pulmonary valve, L-transposition of the great arteries, dextrocardia, double outlet left ventricle, hypoplastic anatomical right ventricle, valvular aortic stenosis and tracheomalacia. We performed anatomical left ventricle to pulmonary artery shunt using an 8-mm expanded polytetrafluoroethylene bicuspid-valved conduit, pulmonary artery plication, and tracheostomy. The patient was discharged in a stable condition while waiting for the Glenn procedure until getting her parent's permission.