Comment
Pulmonary artery aneurysms are found in approximately 1 in 14,000
autopsies, with most being asymptomatic, but some causing symptoms that
can develop life-threatening complications.4 Many
times, patients with pulmonary artery aneurysms have other cardiac or
large vessel anomalies, but there are few cases reported on isolated
pulmonary valve disease in association with pulmonary artery
aneurysms.4, 5 Our patient is unique due to her
Alpha-1 Antitrypsin Deficiency. She successfully underwent replacement
of her pulmonary artery aneurysm with an interposition graft without
complications.