Conclusion
The retroaortic left brachiocephalic vein is a rare congenital systemic venous anomaly, usually associated with malformations involving the outflow tracts. It is also strongly associated with aortic arch anomalies, such as right aortic arch and cervical aortic arch, patent arterial duct, coarctation of aorta, and distal aortic arch aneurysms. Although it does not cause clinical symptoms, knowledge of its presence is important when surgical interventions are required in patients with congenitally malformed hearts, especially in the setting of tetralogy of Fallot, a functionally univentricular heart, right aortic arch, and other aortic arch anomalies.