Total anomalous pulmonary venous connection is a rare congenital anomaly, and has four anatomical subtypes of which the mixed type represents diagnostic and therapeutic challenge. Herein, we present a rare case of obstructed mixed type total anomalous pulmonary venous connection with successful surgical repair

Situs inversus totalis associated with partial anomalous pulmonary venous connection is a very rare congenital heart malformation. Herein, we describe successful surgical repair of the case of a 30-month-old girl who had situs inversus totalis, partial anomalous pulmonary venous connection , large atrial septal defect, and severe pulmonary hypertension.