Background: The association of double aortic arch and common arterial trunk is extremely rare. The initial surgical approach depends on the patient’s clinical condition and associated cardiac anomalies. Aim: To report a rare association of common arterial trunk with double aortic arch in a 4-month-old female infant. Methods: description of case of a rare association where double aortic arch was not diagnosed initially, surgical repair was done successfully. Results and conclusions: associated cardiovascular anomalies may have an impact on management and outcome. Magnetic resonance imaging and computed tomography may be useful in assessment of this rare association. Complete repair has favorable outcome.

We present two patients with history of recurrent respiratory infections, fatigue and sweating. They were diagnosed with absence of connection between the main pulmonary artery (MPA) and right pulmonary artery (RPA) and bilateral ductus arteriosus, with the RPA originating from the ductus arteriosus. Treatment was approached with a hybrid strategy: percutaneous intraluminal angioplasty with a right intraductal stent and device closure of the left ductus arteriosus and followed by surgical reconstruction with interposition of a graft from RPA to MPA. Both patients had a favorable outcome.