Abstract
Unroofed coronary sinus syndrome is a rare congenital heart defect representing less than 1% of all atrial septal defect types, and may be associated with persistent left superior vena cava which may be missed during preoperative diagnosis. Herein, we present a case of a 2-year-old patient who underwent an operation for repair of a coronary sinus-type ASD; however, PLSVC was detected intraoperatively. An antra-atrial tunnel was created to divert the flow of PLSVC into the right atrium along with the repair of the atrial septal defect.
Keywords : persistent left superior vena cava, unroofed coronary sinus, intra-atrial tunnel.