Abstract
Unroofed coronary sinus syndrome is a rare congenital heart defect
representing less than 1% of all atrial septal defect types, and may be
associated with persistent left superior vena cava which may be missed
during preoperative diagnosis. Herein, we present a case of a 2-year-old
patient who underwent an operation for repair of a coronary sinus-type
ASD; however, PLSVC was detected intraoperatively. An antra-atrial
tunnel was created to divert the flow of PLSVC into the right atrium
along with the repair of the atrial septal defect.
Keywords : persistent left superior vena cava, unroofed coronary
sinus, intra-atrial tunnel.