Summary
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is considered a rare and very fatal congenital coronary artery anomaly. It is estimated that this congenital abnormality affects 1 of every 300,000 live births and accounts for 0.25% of all congenital heart defects worldwide. ALCAPA manifests itself most commonly in infant population and it has a 1-year mortality rate of approximately 90%, therefore it is not often considered a diagnosis in the adult population (4, 5). When it presents in adult it is considered an important cause of sudden cardiac death (1, 2). We describe a patient in whom this anomaly was diagnosed during cardiac catheterization for evaluation of progressive shortness of breath and mild to moderate mitral regurgitation founded on a transthoracic echocardiogram (3).