Background and aim of the study: Atrial myxomas are the most common primary cardiac tumors and are generally discovered as incidental findings. When obstructive symptoms become manifest, acute hemodynamic impairment may occur with the necessity of surgical correction. Results: We describe a case of a young woman with progressive dyspnea and syncope, and presence of a huge intracardiac mass. The mass completely obliterated the mitral valve orifice requiring emergent surgery. Immediately following excision and at follow-up normal hemodynamics were restored. Conclusions: Whenever huge intracardiac masses cause hemodynamic compromise, emergent surgery is necessary. Immediate relief is seen following excision.