ACA, anti centromere antibody; RNAPIII, RNA polymerase III; lcSSc, limited cutaneous systemic sclerosis; mRSS, modified Rodnan skin score; PAH, pulmonary arterial hypertension; ILD, interstitial lung disease; GIS, gastrointestinal system; DU, digital ulcer; SRC, scleroderma renal crisis; ANA, antinuclear antibody
Table 4. Clinical features of the patients who were positive only for uncommon scleroderma-specific autoantibodies