We herein report an exceedingly rare case of Evans syndrome with associated tubercular pleural effusion. The patient was initially treated as autoimmune hemolytic anemia. However, the development of thrombocytopenia led to the subsequent diagnosis of Evans syndrome. The co-existence of tuberculosis resulted in additional difficulty during treatment with immunosuppressive medications.

Chylothorax is a well-recognized but uncommon complication during the postoperative period following the repair of left congenital diaphragmatic hernia. Conservative management with close monitoring of chylothorax output and patient status seems superior to surgery in managing this complication.