Aortopulmonary window (APW) is a rare but serious congenital cardiac malformation, most patients with APW will die from congestive heart failure a few months after birth. However, in this case we presented is an extremely rare condition that consist of a type III APW and a ductus arteriosus originated left pulmonary artery. Preoperative diagnosis included echocardiography and chest computerized tomography revealed anatomical structure of the heart and great vessel clearly, cardiac catheterization indicated that the pulmonary resistances indices were 2.92 wood U⁄m^2 in LPA and 3.35 wood U⁄m^2 in RPA, Qp:Qs was 3.26. This patient underwent surgical correction at the age of 9 and successfully survived.