loading page

Stapes Surgery in Osteogenesis Imperfecta: Retrospective Analysis of 18 Operated Ears
  • +2
  • Mohamad Hijazi,
  • Sorina-Dana Mihailescu,
  • Julien Horion,
  • Alice Goldenberg,
  • Jean Paul Marie
Mohamad Hijazi
University Hospital Centre Rouen

Corresponding Author:hijazi.mohamad@outlook.com

Author Profile
Sorina-Dana Mihailescu
University Hospital Centre Rouen
Author Profile
Julien Horion
University Hospital Centre Rouen
Author Profile
Alice Goldenberg
University Hospital Centre Rouen
Author Profile
Jean Paul Marie
Rouen University Hospital
Author Profile

Abstract

Objective : To evaluate short and long term results of stapes surgery in patients with Osteogenesis imperfecta (OI). Design: Retrospective case series. Setting: Tertiary referral center Patients: 18 primary stapes surgeries were performed in 11 hearing-impaired OI patients with evidence of stapes fixation. Intervention: Mainly CO2 laser stapedotomy with Teflon piston prosthesis. Main Outcome Measures: Pre-operative and post-operative audiograms at one month and at least one year Results: The main operative findings were stapes fixation, thickened footplate and fragile or fractured stapes crura. No revision surgery was necessary. Hearing improvement was achieved in 94% of the cases. We obtained an air-bone gap closure to within 10 dB in 46% of the cases and to within 15dB in 92% of the cases at one year follow up. The mean hearing gain in air conduction (at 0.5, 1, 2 and 4 kHz) was 18.4 dB at one month and 22.4 dB at one year. Conclusion: Stapes surgery in OI gives good results with few complication in our series. A hearing gain is often obtained in spite of the sensorineural hearing loss caused by the natural progression of the disease
12 Jan 2021Published in European Archives of Oto-Rhino-Laryngology. 10.1007/s00405-020-06581-9