Arrhythmogenic cardiomyopathy (AC) is a rare inherited myocardial disorder, a cause of sudden death in young people and atheletes; biventricular involvement is often involved. We report on a case of AC diagnosed with multimodality imaging, including transthoracic echocardiography (TTE), two-dimensional strain echocardiography (2DSE), real-time three-dimensional echocardiography (RT-3DE) and cardiac magnetic resonance (CMR) imaging. Especially, combination of 2DSE and RT-3DE was utilized in the diagnosis of AC. In a word, we review the cardiac anomalies associated with AC by multiple imaging techniques and highlight the supplementary role of new echocardiography techniques diagnosing AC when CMR contraindications exist for AC patients.