Introduction:
Scimitar syndrome is a rare pulmonary venolobar syndrome that is
characterized by anomalous pulmonary vein (PV) drainage of the right
lung, most frequently into the inferior vena cava. Associated congenital
abnormalities include right lung hypoplasia and cardiac dextroposition,
with or without structural heart defects. We describe a case of a
patient with Scimitar syndrome and severe chronic heart failure with
left bundle branch block (LBBB) who underwent cardiac resynchronization
therapy with His-bundle pacing (His-CRT), resulting in significant
improvements in functional capacity and left ventricular (LV) function.
To the best of our knowledge, this is the first reported case of His-CRT
in Scimitar syndrome. We highlight the contribution of integrated
imaging modalities to guide accurate lead positioning.