Congenital superior vena cava (SVC) stenosis and obstructed supracardiac
total anomalous pulmonary venous connection (TAPVC) - A surgical
perspective
Abstract
Congenital superior vena cava (SVC) stenosis is a very rare anomaly
especially in pediatric population. Co-existence with obstructed
supracardiac total anomalous pulmonary venous connection (TAPVC) has
never been reported. Clinical examination should prompt detailed and
focused evaluation for this treatable etiology. SVC stenosis, although
causing SVC syndrome, may decrease the severity of pulmonary venous
hypertension by limiting the amount of blood in obstructed common
chamber. Pericardial patch augmentation can cure SVC stenosis, and may
allow for growth potential as well. We describe a case of congenital SVC
stenosis in a case of obstructed supra-cardiac TAPVC in a 3 month old
infant, managed successfully.