A 26 years old lady presented to us with primary amenorrhoea. On examination and investigation she was found to have MRKH syndrome with Situs inversus totalis. Likewise what we do for these syndromic patients, we did sigmoid vaginoplasty. This is one of the uncommon anatomical variants we encountered in our series of cases. Our literature search did not reveal such patient undergoing sigmoid vaginoplasty and so is this case presented for publication.