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SURGICAL MANAGEMENT OF RARE TUMORS (Part 1)
  • +7
  • Alyssa Stetson,
  • Saurabh Saluja,
  • Danielle B. Cameron,
  • Sara Mansfield,
  • Stephanie F. Polites,
  • Joshua Honeyman,
  • John P. Dahl,
  • Mary Austin,
  • Jennifer Aldrink,
  • Emily Christison-Lagay
Alyssa Stetson
Massachusetts General Hospital Department of Surgery
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Saurabh Saluja
The Hospital for Sick Children Division of General and Thoracic Surgery
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Danielle B. Cameron
Massachusetts General Hospital Department of Surgery
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Sara Mansfield
Nationwide Children's Hospital
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Stephanie F. Polites
Mayo Clinic Division of Pediatric Surgery
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Joshua Honeyman
Memorial Sloan Kettering Cancer Center
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John P. Dahl
University of Washington Division of Pediatric General Surgery
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Mary Austin
The University of Texas MD Anderson Cancer Center
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Jennifer Aldrink
Nationwide Children's Hospital
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Emily Christison-Lagay
Yale New Haven Children's Hospital

Corresponding Author:emily.christison-lagay@yale.edu

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Abstract

With an annual cumulative occurrence of approximately 15,000 in North America, all childhood cancers are rare. Very rare cancers as defined by both the European Cooperative Study Group for Rare Pediatric Cancers (EXPeRT) and the Children’s Oncology Group (COG) fall into two principal categories: those so uncommon (fewer than 2 cases/million) that their study is challenging even through cooperative group efforts (e.g. pleuropulmonary blastoma, desmoplastic small round cell tumor) and those that are far more common in adults and therefore rarely studied in children (e.g. thyroid, melanoma, gastrointestinal stromal tumor). [1](#ref-0001) Treatment strategies for these latter tumors are typically based on adult guidelines, although the pediatric variants of these tumors may harbor different genetic signatures and demonstrate different behavior. If melanoma and differentiated thyroid cancer are excluded, other rare cancer types account for only 2% of the cancers in children aged 0 to 14.[1](#ref-0001) This article highlights several of the most common rare tumor types.
11 Jun 2024Submitted to Pediatric Blood & Cancer
12 Jun 2024Submission Checks Completed
12 Jun 2024Assigned to Editor
12 Jun 2024Review(s) Completed, Editorial Evaluation Pending
12 Jun 2024Reviewer(s) Assigned
17 Jun 2024Editorial Decision: Revise Minor
07 Aug 2024Submission Checks Completed
07 Aug 2024Assigned to Editor
07 Aug 20241st Revision Received
08 Aug 2024Review(s) Completed, Editorial Evaluation Pending
09 Aug 2024Reviewer(s) Assigned
10 Aug 2024Editorial Decision: Accept